Unlabelled: Foix-Alajouanine syndrome is an arteriovenous malformation causing subacute congestive myelopathy that can lead to progressive paraplegia. It typically affects the lower thoracic and lumbosacral levels. Arteriovenous fistula (AVF) leads to increased venous pressure, decreasing the arteriovenous pressure gradient and leading to a decrease in spinal cord perfusion, oedema and necrosis. Early recognition and surgical intervention can result in a good prognosis.
Learning Points: Spinodural arteriovenous fistula (SDAF) can present with longitudinally extensive transverse myelitis (LETM), progressive gait instability, and lower extremity weakness.Failure to promptly recognize this condition and misdiagnosis can result in a poor outcome.Microsurgical obliteration of the SDAF provides better results than embolization.
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http://dx.doi.org/10.12890/2020_002063 | DOI Listing |
Ann Med Surg (Lond)
November 2024
Departemnt of Neurosurgery, Cairo University Hospital, Cairo, Egypt.
J Neurosurg Case Lessons
November 2024
Department of Neurosurgery, Faculty of Medicine, University of Tsukuba, Tsukuba, Ibaraki, Japan.
Background: Venous hypertensive myelopathy (VHM), formerly known as "Foix-Alajouanine syndrome," is a spinal cord dysfunction caused by impaired perfusion of the spinal cord. Most cases are attributed to spinal dural arteriovenous fistulas (dAVFs), but there are scattered reports of VHM without concomitant dAVF. Furthermore, no cases of VHM associated with intracranial hemorrhage exist.
View Article and Find Full Text PDFZh Nevrol Psikhiatr Im S S Korsakova
August 2024
Federal Scientific and Educational Center of Medical and Social Expertise and Rehabilitation named after G.A. Albrecht, St. Petersburg, Russia.
The Foix-Alajouanine syndrome was originally reported by these authors in 1926, as rapidly progressive vasculitis on the background of a viral infection. The pathology was represented by the huge, more than 10 times, dilation either of the lumen, or the walls of the spinal vessels, either of the arteries, or the veins. There were no signs of thrombosis, no malformations.
View Article and Find Full Text PDFArq Neuropsiquiatr
September 2024
Universidade Federal de Pernambuco, Centro de Ciências Médicas, Divisão de Neuropsiquiatria, Recife PE, Brazil.
Eur Neurol
August 2024
Department of Neurology, Instituto de Neurologia de Curitiba, Curitiba, Brazil.
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