AI Article Synopsis
- A 9-year-old girl exhibited symptoms such as fevers, cough, nosebleeds, and nasal swelling, leading to the discovery of a nasal mass.
- Imaging with 18F-FDG PET/CT revealed significant disease in her lymph nodes and lungs, as well as unusual FDG uptake in her trachea and bronchial tree.
- Ultimately diagnosed with IgG4-related disease (IgG4-RD), she responded well to treatment; her case is notable as it adds to the limited number of pediatric instances of IgG4-related pulmonary disease reported in medical literature.
Article Abstract
We report the case of a 9-year-old girl who presented with acute fevers, cough, and epistaxis with nasal swelling, and found to have a nasal mass. On 18F-FDG PET/CT, she was found to have marked nodal and pulmonary parenchymal disease with diffuse and symmetrical mural FDG uptake within the trachea and bronchial tree. The differential diagnosis was broad, and she was diagnosed with IgG4-RD (IgG4-related disease) and improved on appropriate treatment. To our knowledge, there are only 2 other pediatric cases of IgG4-related pulmonary disease in the literature, and our case serves as a unique constellation of intrapulmonary IgG4-RD imaging findings.
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