Download full-text PDF |
Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7591321 | PMC |
| http://dx.doi.org/10.1016/j.jdcr.2020.05.032 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
An Unusual Case of Disseminated Erdheim-Chester Disease.
WMJ
July 2024
Medical College of Wisconsin, Milwaukee, Wisconsin.
Introduction: Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytic multisystem disorder, deriving from mononuclear phagocytic cells. It is notoriously challenging to diagnose. Here we present a case of a patient with multisystem ECD.
View Article and Find Full Text PDFCraniospinal irradiation for respiratory failure secondary to central nervous system Erdheim-Chester disease.
Radiat Oncol J
June 2022
Department of Radiation Oncology, The Ohio State University Wexner Medical Center, Columbus, OH, USA.
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis typically featuring lower extremity osteosclerosis (96%) from Langerin-negative histiocytes with fibrosis. Central nervous system (CNS)-only disease is extremely rare, and particularly difficult to diagnose and manage. Neurologic complaints may be refractory to systemic therapy (ST), and the role of radiation therapy (RT) is undefined.
View Article and Find Full Text PDFGeneralized Eruptive Histiocytoma With S100 Protein-Positive Histiocytes and Prominent Eosinophilic Infiltration: A Rare Case Report.
Am J Dermatopathol
July 2022
Department of Dermatology, the Second Xiangya Hospital of Central South University, Changsha, Hunan, China .
Generalized eruptive histiocytoma (GEH) is a very rare benign disorder belonging to the group of non-Langerhans cell histiocytosis (non-LCH). GEH is characterized by a nearly uniform infiltrate of histiocytes with classic immunological phenotype (CD68+, S-100- and CD1a-). Prominent eosinophilic infiltration and S100-positive histiocytes are rarely associated in GEH.
View Article and Find Full Text PDFSystemic and Craniospinal Rosai Dorfman Disease with Intraparenchymal, Intramedullary and Leptomeningeal Disease.
Int J Hematol Oncol Stem Cell Res
October 2021
Department of Radiology and Biomedical Imaging, University of California San Francisco, San Francisco, California, United States.
Rosai Dorfman disease is a rare histiocytic disorder of over-production of non-Langerhans histiocytes, which typically manifests with massive lymphadenopathy and sinonasal involvement. We report a rare case of systemic and disseminated craniospinal Rosai Dorfman disease with intraparenchymal and leptomeningeal involvement, but no sinus or dural-based disease. The diagnosis was established by biopsy of a hypothalamic mass.
View Article and Find Full Text PDFNecrobiotic Xanthogranuloma - Case Report and Literature Review.
Curr Health Sci J
March 2021
Department of Pathology, Emergency County Hospital, Craiova, University of Medicine and Pharmacy of Craiova, Romania.
Necrobiotic xanthogranuloma is a rare type of non-Langerhans histiocytosis, whose main clinical features are the development of red-brown, purplish or yellowish skin papules and nodules, which evolve by forming infiltrated plaques. The periorbital region is the most commonly affected site. Some cases have lesions on the torso or extremities, with no facial involvement.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!