Spondylectomy for Primary Ewing Lumbar Sarcoma in Children.

Rev Bras Ortop (Sao Paulo)

Department of Orthopedic Surgery, Hospital de São João, Faculdade de Medicina, Universidade do Porto, Porto, Porto, Portugal.

Published: October 2020

Primary Ewing sarcoma in the spine is very rare, and the treatment for it is multidisciplinary. There is no consensus regarding the optimal method of local control; however, en bloc resection is associated with an improvement in survival rates. The authors report a case of a 5-year-old girl who initially presented low back pain, and was diagnosed with Ewing sarcoma after being submitted to imaging studies by radiography, magnetic resonance and bone biopsy. A spondylectomy was performed in accordance with the Euro Ewing protocol. At the three-year follow-up, the patient had no restrictions regarding her daily activities, and there has been no evidence of recurrence to date.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7575362PMC
http://dx.doi.org/10.1016/j.rboe.2017.10.010DOI Listing

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