Introduction: Vascular Ehlers Danlos syndrome is a rare connective tissue disease that is associated with various arterial complications.
Report: A 25 year old man with vascular Ehlers Danlos syndrome presented with acute lower back pain as a result of a ruptured aneurysm of the median sacral artery (MSA). Prior medical history included several vascular events resulting in a right iliac occlusion. The unusual location of aneurysmal disease of the MSA might be explained by extensive collateral flow recruitment due to this occlusion.
Conclusion: Previous vascular events inducing collateral recruitment might justify a more frequent follow up in patients with connective tissue disorders.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7320209 | PMC |
| http://dx.doi.org/10.1016/j.ejvssr.2019.12.002 | DOI Listing |
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