Introduction: Langerhans cell histiocytosis is a rare disease. When it occurs in the cranium/facial bones, the mandibular location is the most frequent.
Presentation Of Case: A 31 years-old man was referred to our department for a mandibular chronic discomfort during an acute exacerbation, a pathologic mandibular fracture.The diagnosis was confirmed by a subsequent CT scan. Histological and immunohistochemistry analysis of the maxillary and mandibular cystic lesions Langerhans cell histiocytosis of the oral cavity.
Discussion: This is a case of rare single system LCH at two distinct locations: one at the mandibular bone and the other at the upper left maxilla. Both were uncovered by an acute exacerbation of a chronic discomfort secondary to a mandibular pathologic fracture. This should draw attention to the issues of the diagnosis.
Conclusion: An early LCH diagnosis and a multidisciplinary treatment plan allow the improvement of the patient 's prognosis and quality of life.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7327002 | PMC |
| http://dx.doi.org/10.1016/j.amsu.2020.06.019 | DOI Listing |
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