Unlabelled: Neurofibromatosis type 1 (NF1) is a clinically heterogeneous neurocutaneous genetic disorder that manifests in the form of coffee-milk spots on the skin, Lish nodules, lentigines on the underarms and on the inguinal region, and neurofibromas. Orofacial manifestations of NF1 are common. Through a review of the literature, bone lesions, orthodontic and dental abnormalities, periodontal manifestations, and caries related to NF1 will be explored. In this study, we present a clinical case of a patient with neurofibroma in the oral cavity and infraocclusion of primary molars, as well as his dental management.
How To Cite This Article: Wotjiuk F, Hyon I, Dajean-Trutaud S, Dental Management of Neurofibromatosis Type 1: A Case Report and Literature Review. Int J Clin Pediatr Dent 2019;12(6):577-581.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7229384 | PMC |
| http://dx.doi.org/10.5005/jp-journals-10005-1668 | DOI Listing |
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