Bilateral Tessier no. 7 clefts are rarely reported in the literature. Here, we describe the presence of accessory maxilla with supernumerary teeth in a patient who exhibited bilateral Tessier no. 7 clefts; the diagnosis was established based on the patient's history, clinical presentation, and computed tomography images. A review of the available literature revealed 24 patients with Tessier no. 7 clefts from 2000 to 2020, including our patient. The most common clinical manifestation in patients with Tessier no. 7 clefts comprises bilateral facial clefts. Additionally, Tessier no. 7 clefts are more frequently found in boys or men, rather than in girls or women. The presence of an accessory maxilla with supernumerary teeth in a patient with bilateral Tessier no. 7 clefts is extremely rare. Early detection of craniofacial abnormalities is important, because it may influence patient prognosis and management.
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http://dx.doi.org/10.1177/0300060520925680 | DOI Listing |
Neurosurg Focus
January 2025
3ENT and Head and Neck Research Center and Department, The Five Senses Health Institute, School of Medicine, Iran University of Medical Sciences, Tehran, Iran.
Objective: Craniofacial clefts, characterized by congenital disruptions in the development of facial and cranial tissues, often present alongside orbital hypertelorism (ORH), an abnormal increase in the interorbital distance. These conditions pose significant challenges in craniofacial surgery due to the complex anatomical and functional considerations involved. This single-center cohort study retrospectively analyzed 22 patients diagnosed with craniofacial cleft syndromes and ORH who were treated at the Craniofacial Centre, Fatima Plastic and Reconstructive Surgery Hospital between July 2016 and October 2023.
View Article and Find Full Text PDFCleft Palate Craniofac J
November 2024
Department of Plastic Surgery, Cleft and Craniofacial Center, Shizuoka Children's Hospital, Shizuoka, Japan.
A true median cleft is an extremely rare congenital anomaly characterized by a midline vertical cleft and various deformities, also known as Tessier number 0 cleft. Here we report a case of a 5-year-old Asian boy with true median cleft associated with sinus tracts in the nasal septum, a phenomenon not previously reported in the literature. The tracts were identified as the cause of recurrent infections around the oral vestibule and upper lip.
View Article and Find Full Text PDFCureus
October 2024
Plastic and Reconstructive Surgery, SRM Medical College Hospital and Research Centre, Chennai, IND.
Tessier 7 cleft, or transverse facial cleft, is a rare congenital anomaly involving lateral facial tissues, often resulting from embryonic disruptions in the first and second branchial arches. It presents varying severities from macrostomia to complete clefts affecting soft tissue and skeletal structures. Surgical management is challenging, requiring a multidisciplinary approach for functional and aesthetic reconstruction.
View Article and Find Full Text PDFJ Plast Reconstr Aesthet Surg
October 2024
Burns & Plastic Surgery Center, Hayatabad Medical Complex, Peshawar, Pakistan.
Background: Standardization of surgical protocols is an evolving issue owing to the low incidence of rare craniofacial clefts. In this article, we present our surgical management technique for repair of rare craniofacial clefts and evaluate the postoperative results.
Methods: This study was conducted from 2013 to 2022 and included patients who presented with craniofacial clefts.
Indian J Otolaryngol Head Neck Surg
August 2024
Department of Neonatology, All India Institute of Medical Sciences, Bhopal, Bhopal, Madhya Pradesh 462020 India.
A term newborn was detected for a rare facial defect in the delivery room. The defect arose due to malunion along the lines of facial development during fetal life. This embryonic defect is classified according to the areas of face involved and its associated structures.
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