Dysplasia epiphysealis hemimelica (DEH) or Trevor's disease is a rare developmental disorder of asymmetric epiphyseal cartilage overgrowth accompanied by an accessory, epiphyseal ossification center. No published reports exist of metacarpal or phalangeal DEH. We report a case of bilateral DEH of the index finger: right-sided distal index metacarpal and left-sided index proximal phalanx. Both were surgically corrected with excision of the accessory ossification center; a transepiphyseal cartilaginous wedge was excised, and the articular surface was maintained. Follow-up shows maintenance of alignment without recurrence at 12 and 18 months after operation.
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Arthroscopic Management of Dysplasia Epiphysealis Hemimelica (Trevor Disease) of the Ankle.
Arthrosc Tech
August 2024
Tuen Mun Hospital, Hong Kong SAR, China.
Dysplasia epiphysealis hemimelica (Trevor disease) is a rare skeletal development disorder of childhood, characterized by irregular ossification centers, which may develop together or individually, leading to asymmetric epiphyseal cartilage overgrowth, affecting 1 side of the epiphyses or the epiphyses equivalents (the medial side being affected twice as often as the lateral), until skeletal maturity is reached. Trevor disease around the ankle is locally aggressive with a poor outcome, especially in tumors involving the articular surface. The purpose of this Technical Note is to describe the details of arthroscopic management of dysplasia epiphysealis hemimelica (Trevor disease) of the ankle.
View Article and Find Full Text PDFDysplasia Epiphysealis Hemimelica (Trevor Disease) of the Talus in a Toddler: A Case Report With a Long Follow-up.
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July 2024
IRCCS Istituto Ortopedico Rizzoli, 1st Orthopaedics and Traumatologic Clinic, Bologna, Italy.
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View Article and Find Full Text PDFUnveiling dysplasia epiphysealis hemimelica (Trevor's disease) in the foot and ankle: A systematic review.
J Orthop
June 2024
IRCCS Istituto Ortopedico Rizzoli, Via Giulio Cesare Pupilli 1, 40136, Bologna, Italy.
Background: Dysplasia epiphysealis hemimelica is a rare non-inherited condition characterized by the unilateral predominance of osteochondromas in one or more epiphyses, with ankles and knees being the most affected joints. Treatment approaches vary based on the localization of the disease, encompassing both conservative and surgical options. Due to its rarity, there is a lack of definitive surgical guidelines or specific treatment modalities.
View Article and Find Full Text PDFIsolated Dysplasia Epiphysealis Hemimelica (Trevor Disease) of the Acetabulum: Literature Review.
J Am Acad Orthop Surg Glob Res Rev
October 2023
From the Department of Orthopaedic Surgery, The Johns Hopkins University, Baltimore, MD.
Dysplasia epiphysealis hemimelica (DEH), also known as Trevor disease, is a rare pathologic proliferation of cartilage with unknown etiology creating cartilaginous osteochondroma exostoses intra-articularly or juxta-articularly. Herein, we reviewed the literature about acetabular osteochondroma in children and report a case of a 9-year-old boy who presented to the orthopaedic clinic with complaints of gait disturbance, right hip discomfort, and with increasing severity and frequency of hip subluxation episodes over the course of a year. Imaging studies revealed dysplasia of the right hip with subluxation secondary to acetabular lesion.
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