In this case, we present a patient with unilateral salivary gland enlargement and periorbital edema with erythematous rash. We discuss the differential diagnosis and the relevant therapy.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC7045927 | PMC |
| http://dx.doi.org/10.31138/mjr.28.1.57 | DOI Listing |
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Idiopathic Inflammatory Myopathies are rare conditions with several heterogeneous disease subtypes. They can range from limited muscle or skin involvement to severe, systemic, life-threatening disease. Although the etiology is unknown, some evidence suggests a role for external agents, particularly drugs.
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Department of Neurology, Tokushima University Hospital, Japan.
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[Two cases of anti-nuclear matrix protein 2 antibody-positive dermatomyositis sine dermatitis with severe diffuse subcutaneous edema and dysphagia].
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Centre for Musculoskeletal Research, Division of Musculoskeletal & Dermatological Sciences, The University of Manchester Faculty of Biology Medicine and Health, Manchester, UK.
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J Investig Med High Impact Case Rep
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