Desmoid tumors, also known as aggressive fibromatoses, are clinically rare soft-tissue tumors that arise from such connective tissues as the musculoaponeurotic structures. The majority of the reported intra-abdominal desmoid tumors occur in the small intestinal mesentery and peritoneum, whereas stomach desmoid tumors are extremely rare. The present study reports a case of stomach desmoid tumor and reviews the related available literature. The diagnosis of the stomach desmoid tumors can be made with routine pathological and immunohistochemical examinations. Compared with desmoid tumors at other sites, the currently preferred treatment of the stomach desmoid tumors with negative margins is radical resection of tumors. All the follow-ups of patients with the stomach desmoid tumors show no obvious recurrence, suggesting that the prognosis of the stomach desmoid tumors is good.
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