Meningioangiomatosis is a rare histologically distinct abnormality that is occasionally associated with intracranial meningioma. The rhabdoid variant of meningioma is also uncommon and is classified as a World Health Organization Grade III tumour. We report a case of meningioangiomatosis in conjunction with a meningioma with prominent rhabdoid features, in an infant male who underwent complete surgical resection of the lesion. The patient has been followed up for 6 years with no disease recurrence. To our knowledge, this is the first report in the literature describing meningioangiomatosis combined with a meningioma with rhabdoid features.

Download full-text PDF

Source
http://dx.doi.org/10.1007/s00381-019-04486-5DOI Listing

Publication Analysis

Top Keywords

meningioma rhabdoid
12
rhabdoid features
12
meningioma
5
features combined
4
meningioangiomatosis
4
combined meningioangiomatosis
4
meningioangiomatosis infancy
4
infancy novel
4
novel combination
4
combination meningioangiomatosis
4

Similar Publications

Background: Central nervous system (CNS) tumors lead to cancer-related mortality in children. Genetic ancestry-associated cancer prevalence and outcomes have been studied, but is limited.

Methods: We performed genetic ancestry prediction in 1,452 pediatric patients with paired normal and tumor whole genome sequencing from the Open Pediatric Cancer (OpenPedCan) project to evaluate the influence of reported race and ethnicity and ancestry-based genetic superpopulations on tumor histology, molecular subtype, survival, and treatment.

View Article and Find Full Text PDF
Article Synopsis
  • Pediatric intracranial tumors at the skull base are rare, challenging to treat due to complex anatomy, and lack substantial clinical evidence, prompting a study on surgical approaches and outcomes.
  • The study involved 12 children under 18 who underwent skull base surgery from 2017 to 2023, analyzing demographics, tumor details, surgical methods, and survival rates.
  • Results indicated a predominance of female patients, varying tumor locations and types, with 58.3% achieving gross or near-total resection; however, 33.3% of patients died from tumor progression within an average of 15 months.
View Article and Find Full Text PDF

Neuropathology Entities Involving the Sinonasal Tract.

Surg Pathol Clin

December 2024

Department of Pathology & Immunology, Division of Neuropathology, Washington University School of Medicine, 660 South Euclid Avenue, St. Louis, MO 63110, USA. Electronic address:

Article Synopsis
  • Neuropathologic entities, though rare, can affect the sinonasal tract through different mechanisms including embryological defects and ectopic tissue remnants.
  • These entities may also arise from benign tumors that extend from the brain or nearby structures, such as pituitary adenomas and meningiomas.
  • Additionally, high-grade intracranial tumors like glioblastomas can invade the sinonasal area, making it essential for surgical pathologists to include these in the differential diagnoses of unusual sinonasal lesions.
View Article and Find Full Text PDF
Article Synopsis
  • - Non-neuroendocrine tumors make up about 10% of primary tumors in the sella, with a variety of unusual, benign, and aggressive types present.
  • - The review focuses on key characteristics of tumors related to the posterior pituitary gland and specific types like infundibulum tumors and atypical rhabdoid teratoid tumors.
  • - It provides essential information for diagnosing and managing these tumors, highlighting their clinicopathological features.
View Article and Find Full Text PDF

Introduction: Spinal tumors (ST) often result in dire prognosis, carrying risks such as permanent paralysis, sensory loss, and sphincter dysfunction. Data on their incidence and etiology in pediatric populations are markedly scant. Our study investigates the etiology, clinical manifestation, treatment, and outcomes of pediatric ST.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!