• Danon disease is a rare X-linked genetic disorder of the gene. • Danon cardiomyopathy has a high incidence of preexcitation and severe LVH. • mutation–associated cardiomyopathy can mimic sarcomeric HCM. • Multimodality imaging is key to a successful diagnosis of Danon disease.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6833129PMC
http://dx.doi.org/10.1016/j.case.2019.04.007DOI Listing

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