Schwannomas of the eighth cranial nerve are benign tumours commonly found in the internal auditory meatus or in the cerebellopontine angle. In most cases, they arise from the inferior or vestibular portion of the vestibular nerve. Rarely, these tumours present in the inner ear and are then called intralabyrinthine schwannomas. Bilateral schwannomas are known in neurofibromatosis type 2 (NF2). Bilateral and ipsilateral, multilocular sporadic schwannomas of the eighth cranial nerve have been described as extremely rare findings. This report describes the first case of bilateral sporadic intracochlear schwannomas in a patient with no genetic or clinical features of NF2.
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Pediatric Intracochlear Schwannoma: Case Series and Review of the Literature.
J Int Adv Otol
November 2024
The Department of Medicine and Surgery, University of Parma, Parma, Italy.
Background: Intracochlear schwannomas (ICSs) are a subtype of intralabyrinthine schwannomas, completely located in the cochlear lumen. ICSs are particularly rare in the pediatric population. Putative diagnosis is made on the basis of magnetic resonance findings with signal characteristics that should remain the same at follow-up imaging.
View Article and Find Full Text PDFClinico-Radiological Manifestations of Cochlear Schwannomas.
J Audiol Otol
October 2024
Departments of Otorhinolaryngology, Yonsei University College of Medicine, Seoul, Korea.
Background And Objectives: Cochlear schwannomas, which are categorized into intracochlear and intravestibulocochlear schwannomas (ICs and IVCs, respectively) are rare and may cause hearing loss (HL). The affected region is invariably correlated with tumor location, which can be detected on magnetic resonance imaging (MRI). We describe the cochleovestibular manifestations of ICs and IVCs.
View Article and Find Full Text PDFRevised Classification of Inner Ear Schwannomas.
Otol Neurotol
January 2025
Department of Otolaryngology-Head and Neck Surgery, Mayo Clinic, Rochester, Minnesota, USA.
Article Synopsis
- Over the past two decades, there has been a growing focus on diagnosing and managing inner ear schwannomas, especially regarding hearing rehabilitation through cochlear implants, but the terminology used to classify these tumors has been inconsistent and complex.
- At the Ninth Quadrennial Conference in May 2023 in Bergen, Norway, experts reached a consensus to standardize terminology, ultimately agreeing on the term "inner ear schwannoma (IES)" to clearly describe tumors affecting the eighth nerve in the cochlea, vestibule, or semicircular canals.
- The newly established classifications break down these tumors into three complexity levels: low (intravestibular, intracochlear), intermediate (with internal
Detecting endolymphatic hydrops in patients with cranial nerve VIII schwannoma using hydrops MR examination.
Eur Arch Otorhinolaryngol
October 2024
Departments of Otolaryngology, National Taiwan University Hospital, Taipei, Taiwan.
Purpose: This study utilized Hydrops MRI in patients with cranial nerve (CN) VIII schwannoma to assess the concomitance with endolymphatic hydrops (EH), aiming to elucidate the mechanism of hydrops formation in these patients.
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Electrocochleography-Based Tonotopic Map: I. Place Coding of the Human Cochlea With Hearing Loss.
Ear Hear
December 2024
Department of Otolaryngology-Head and Neck Surgery, Washington University School of Medicine in St. Louis, St Louis, Missouri, USA.
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- - The study aims to map the tonotopy (frequency organization) of the human cochlea in vivo using cochlear implant electrodes, addressing challenges of past research that relied on cadaver and animal models.
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