Dermatomyositis: An Acute Flare and Current Treatments.

Clin Med Insights Case Rep

Department of Pharmacy, West Jefferson Medical Center, Marrero, LA, USA.

Published: June 2019

The purpose of this case report is to assess and review the literature to determine the frequency of occurrence of dermatomyositis (DM). Dermatomyositis is a rare autoimmune condition that disproportionately affects adolescence and pediatric patients. The symptomatology experienced in this condition includes but not limited to fatigue, reduced mobility, and dysphagia. Symptoms of dysphonia and dyspnea have been reported due to weakened esophageal and respiratory muscle. Another major complication seen in DM is calcinosis. Calcinosis is a calcium deposit on soft tissue. This is mostly been attributed to late diagnosis or use of ineffective treatment regimen. Systemic corticosteroid is the first-line treatment for DM; however, other agents such as anti-malaria, IVIG, and immunosuppressive therapies have been used successfully.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6582284PMC
http://dx.doi.org/10.1177/1179547619855370DOI Listing

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