The surgical management of severe truncal valvular dysfunction is still challenging in neonates with persistent truncus arteriosus. This report describes a 14-day-old neonate with severe truncal valve insufficiency successfully undergoing truncal valve repairs, and followed by valve replacement at the age of 4 years. The truncal valve was quadricuspid with two large and two small leaflets, and all leaflets had severe dysplastic and myxomatous changes. We performed leaflet extension and bicuspidization valvuloplasty for this valve. This patient obtained somatic growth for 4 years without heart failure symptoms, and safely underwent prosthetic valve replacement. This technique would be effective for truncal valve dysfunction in neonates as the life-saving and the bridging procedure to valve replacement.
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.1007/s00246-019-02126-y | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Management Strategies for Truncus Arteriosus: A Comparative Analysis of Staged vs. Primary Repair.
Pediatr Cardiol
January 2025
Department of Cardiovascular Surgery, Okayama University Graduate School of Medicine, Dentistry, and Pharmaceutical Sciences and Okayama University Hospital, 2-5-1 Shikatacho, Kitaku, Okayama, Japan.
We reviewed the outcomes of truncus arteriosus repair (primary vs. staged repair incorporating bilateral pulmonary artery banding), focusing on survival, reintervention, and functional data. We analyzed 39 patients who underwent a first intervention for truncus arteriosus (staged, n = 19; primary, n = 20) between 1992 and 2022.
View Article and Find Full Text PDFTruncal valve repair in neonates.
J Thorac Cardiovasc Surg
December 2024
Department of Cardiothoracic Surgery, Royal Children's Hospital, Melbourne, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Australia; Heart Research Group, Murdoch Children's Research Institute, Melbourne, Australia; Melbourne Centre for Cardiovascular Genomics and Regenerative Medicine, Melbourne, Australia. Electronic address:
A rare complex association of truncus arteriosus with anomalous left coronary artery from the pulmonary artery: A case of rare congenital deformity.
Radiol Case Rep
January 2025
Head of Department of Cardiology, Al Bassel Heart Institute, Damascus, Syria.
Anomalous left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital deformity, and its association with truncus arteriosus (TA) has been infrequently described in medical literature. We report a case of a 3-year-old child presenting with failure to thrive and recurrent respiratory infections, who was diagnosed with truncus arteriosus type 1 and an anomalous left coronary artery originating from the pulmonary artery. The embryological basis of both TA and ALCAPA involves disruptions in the normal development of the aorticopulmonary septum and coronary arteries.
View Article and Find Full Text PDFRisk Factors and Outcomes of Perioperative Extracorporeal Membrane Oxygenation in Neonates and Infants Undergoing Truncus Arteriosus Repair.
World J Pediatr Congenit Heart Surg
October 2024
Division of Pediatric Cardiology, Department of Pediatrics, Medical University of South Carolina College of Medicine, Charleston, SC, USA.
Despite surgical advances, neonatal truncus arteriosus repair remains high risk and approximately 10% of patients receive perioperative extracorporeal membrane oxygenation (ECMO). We aimed to assess factors and outcomes associated with the use of perioperative ECMO in infants undergoing truncus arteriosus repair. We conducted a retrospective cohort study of patients who underwent truncus arteriosus repair between 2004 and 2019, using administrative data from the Pediatric Health Information System database.
View Article and Find Full Text PDFSurgical anatomy of aortic root: Toward precise and durable aortic, neo-aortic, and truncal valve repairs.
J Thorac Cardiovasc Surg
October 2024
Department of Cardiac Surgery, The Royal Children's Hospital, Melbourne, Australia; University of Melbourne, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia; Melbourne Children's Centre for Cardiovascular Genomics and Regenerative Medicine, Melbourne, Australia. Electronic address:
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!