Early Onset Primary Adrenal Insufficiency in Males with Adrenoleukodystrophy: Case Series and Literature Review.

J Pediatr

Division of Pediatric Endocrinology and Diabetes, The Children's Hospital at Montefiore, Albert Einstein School of Medicine, Bronx, NY. Electronic address:

Published: August 2019

The lifetime risk for adrenal insufficiency in male children with adrenoleukodystrophy (ALD) is estimated at 80%-86%. Prior to newborn screening, male children with ALD were identified by family history or after symptom development. These young patients with ALD and adrenal insufficiency support newborn screening for ALD.

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http://dx.doi.org/10.1016/j.jpeds.2019.04.021DOI Listing

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