Congenital absence of the pericardium: A rare and challenging diagnosis.

JAAPA

Ayman Elbadawi is a cardiology fellow at the University of Texas Medical Branch in Galveston, Tex. At Rochester (N.Y.) General Hospital, Basarat Baig is a hospitalist, Erfan Alotaki is an internal medicine resident, and Heena Khalid is a hospitalist. Muhammad Khan is a cardiologist at the University of Virginia in Charlottesville, Va. The authors have disclosed no potential conflicts of interest, financial or otherwise.

Published: May 2019

This article describes a patient who presented to the ED after multiple episodes of syncope. His physical examination was unremarkable and an initial workup was negative. Transthoracic echocardiography and chest CT confirmed the diagnosis of congenital complete absence of the pericardium, a rare developmental abnormality most common in men.

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http://dx.doi.org/10.1097/01.JAA.0000554223.33382.c0DOI Listing

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