Objective: To explore the neuropsychological correlates and implications of familial hemiplegic migraines (FHMs).

Background: FMH is a rare, autosomal dominant subtype of migraine that only occurs in 0.01% of the population. Little is known about the neuropsychological impact of FHMs; however, cognitive impairment associated with cerebellar syndrome has been identified in some cases.

Method: A single case study involving a 24-year-old male who recently endured an atypical, prolonged FHM episode.

Results: The patient's overall neuropsychological functioning was intact with low average semantic fluency and processing speed, and mild indications of executive dysfunction.

Conclusion: Baseline and serial neuropsychological testing in individuals with FHM may help identify the potential progression and course of cognitive impairment associated with this condition.

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http://dx.doi.org/10.1111/head.13505DOI Listing

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