A case of papular mucinosis (scleromyxoedema of Arndt-Gottron) in a 64-year-old man is reported. Although a cutaneous mucinosis, the disease is characterized by a number of systemic disorders which determine the course and prognosis of the disease. A survey of 57 reported cases reveals that, in addition to the obligatory paraproteinaemia, neurological (24% of cases), cardiovascular (10%) and myopathic (9%) symptoms are in the foreground. Systemic lymphoplasmo-reticular involvement occurred in 14%. These findings emphasize the need for interdisciplinary cooperation in the diagnosis and for long-term supervision of patients with this disease.
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http://dx.doi.org/10.1055/s-2008-1068538 | DOI Listing |
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