Valve-sparing aortic root and aortic arch replacement in a 5-year-old boy with Loeys-Dietz syndrome.

Eur J Cardiothorac Surg

Department of Pediatric Cardiac Surgery, Pediatric Heart Center Duisburg, University of Duesseldorf, Duesseldorf, Germany.

Published: August 2019

In this study, we describe the case of a 5-year-old boy who presumably presented with Loeys-Dietz syndrome. A huge aneurysm of the ascending aorta and the aortic arch extended beyond the left subclavian artery and was accompanied by a slight narrowing of the aortic isthmus.

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http://dx.doi.org/10.1093/ejcts/ezy446DOI Listing

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