AI Article Synopsis
- Shone syndrome, first described in 1963 by Dr. JD Shone, is a rare group of congenital heart defects that make up about 0.6% of all congenital heart abnormalities.
- It includes specific issues like coarctation of the aorta, subaortic stenosis, supravalvular mitral ring, and a parachute mitral valve.
- The case presented aims to highlight the potential post-surgical imaging characteristics of Shone syndrome using computed tomography.
Article Abstract
Shone syndrome was first described in 1963 by Dr JD Shone. It is a constellation of congenital abnormalities compromising approximately 0.6% of all cases of congenital cardiac abnormalities. Shone syndrome is also known as Shone complex, involving several characteristic cardiac abnormalities: coarctation of the aorta, subaortic stenosis, supravalvular mitral ring, and a parachute mitral valve. Given the uncommon nature of the disease, we present this case to illustrate potential postsurgical appearances of Shone syndrome, specifically on computed tomography imaging.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6223228 | PMC |
| http://dx.doi.org/10.1016/j.radcr.2018.10.004 | DOI Listing |
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