Atypical presentation of a solid-variant orbital aneurysmal bone cyst with a literature review.

Neurochirurgie

School of Medicine, University of Connecticut, 263, Farmington Avenue, Farmington, Connecticut, 06030, USA; Department of Surgery, Division of Ophthalmology, University of Connecticut Health, 263, Farmington Avenue, Farmington, Connecticut, 06030, USA. Electronic address:

Published: December 2018

Introduction: Aneurysmal bone cysts (ABCs) are rare, rapidly expansile, benign, vascular lesions capable of causing local bone destruction. The majority of cases present as multi-cystic lytic lesions (with solid-variant ABCs representing<10% of all presentations) of the long bones or vertebrae, rarely occurring in the head/neck region.

Clinical Case: A 44-year-old female presented with nine days of worsening pain, ptosis and proptosis in the right eye. CT and MR imaging revealed a 3.2cm extra-axial multiloculated right frontal lobe mass in the orbit with fluid-fluid levels secondary to layering of solid blood components. A right craniotomy was performed and the lesion was resected piecemeal with subsequent high speed burring to remove residual tissue. Histological evaluation revealed spindle and giant cell infiltration of the bone without vascular channels. Based on these findings, the lesion was diagnosed as a solid-variant orbital ABC without paranasal sinus involvement. The patient recovered fully with no residual symptoms.

Conclusion: This case report details a rare presentation of ABC (solid-variant presenting outside of the vertebrae/long bones) with discussion concerning possible treatment modalities and guidance for follow-up.

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.neuchi.2018.10.001DOI Listing

Publication Analysis

Top Keywords

aneurysmal bone
8
atypical presentation
4
presentation solid-variant
4
solid-variant orbital
4
orbital aneurysmal
4
bone cyst
4
cyst literature
4
literature review
4
review introduction
4
introduction aneurysmal
4

Similar Publications

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!