Pediatric Primary Ovarian Angiosarcoma: From Rarity to a Realization.

Background: Angiosarcoma is an uncommon high-grade sarcoma in children. Visceral angiosarcoma involving the ovary is extremely rare. Because of the lack of recurrent cytogenetic alterations, histopathological identification of this uncommon tumor in unusual sites like the ovary demands pathologic expertise. Complete surgical resection and radiotherapy are the chief treatment modalities determining survival, with chemotherapy contributing a minor role.

Case: We discuss a 11-year-old prepubertal girl who presented with primary angiosarcoma of the ovary.

Summary And Conclusion: Early realization of such exceptional presentations of these tumors is needed to achieve the best treatment outcome.