[Juvenile retinoschisis and macular hole: a case report].

Juvenile retinoschisis is an inherited macular dystrophy that is transmitted in the chromosome X-linked recessive mode. Clinical signs include a macular star, with or without peripheral retinoschisis, responsible for decreased visual acuity. We report the case of a 12-year-old boy received for a visual acuity decline (VAD). His visual acuity after the best correction is 10/100 on the right and 20/100 on the left. The anterior segment examination shows no peculiarities. In funduscopy, macular striations and macular hole are observed respectivelly on the right and on the left, with inferotemporal schisis in the middle periphery. The electrophysiological assessment shows a major dysfunction of the electroretinogram. The evolution is aggravated by the occurrence of vitreous hemorrhage and retinal detachment.