Superficial siderosis misdiagnosed as idiopathic bilateral neurosensorial deafness.

BMJ Case Rep

Department of Neuroscience, Centro de Investigación Biomédica de Occidente, Instituto Mexicano del Seguro Social, Guadalajara, Mexico.

Published: July 2018

Superficial siderosis (SS) is a rare condition resulting from different sources of bleeding into the subpial space. The most common symptoms are: hypoacusia, ataxia, incontinence, dementia and parkinsonism. Since several neurodegenerative disorders may present with same clinical features, SS is often misdiagnosed. Here we present a case of SS misdiagnosed as idiopathic bilateral neurosensorial deafness.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC6047722PMC
http://dx.doi.org/10.1136/bcr-2017-222639DOI Listing

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