Neuropsychological Difficulties Associated with Dopa Responsive Dystonia.

J Pediatr Neurosci

Leicester Royal Infirmary, Leicester, UK.

Published: January 2018

A young girl with L-dopa responsive dystonia showed significant improvements in motor function but had ongoing complaints of neuropsychological difficulties. A neuropsychological evaluation was undertaken to understand the nature of her difficulties. Intellectual function, attention, executive function, and academic attainment were assessed using published psychometric tests. Verbal and non-verbal reasoning was found to be age appropriate. Particular difficulties were identified with working memory, visual selective attention, dual attention, and processing speed which were having a significant impact upon the child and her family. The importance of a thorough neuropsychological evaluation is discussed in helping to appropriately manage and support the child with this chronic but rare health condition.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5982475PMC
http://dx.doi.org/10.4103/JPN.JPN_142_17DOI Listing

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