Unicentric epithelioid hemangioendothelioma of the calcaneus: a case report and review of literature.

Clin Sarcoma Res

1Department of Orthopaedics, West Virginia University, PO Box 9196, Morgantown, WV 26506-9196 USA.

Published: April 2018

Background: This review of the literature combined with a clinical case will allow the illustration of of this variable malignancy, display a role for limb salvage surgery with intralesional treatment, and offer a clinical example of epithelioid hemangioendothelioma, a rare malignancy.

Case Presentation: The case report presents a case of solitary epithelioid hemangioendothelioma (EHE) of the calcaneus in a 60-year-old male. Primary vascular tumors of the bone are rare; however, EHE is one of the most common primary malignant vascular tumors to occur in bone. A review of the literature found few cases that involved the calcaneus; those cases found that involved the calcaneus were either part of a multifocal or metastatic disease process. Our case -- of solitary EHE in the calcaneus treated with surgical excision by curettage and cementing.

Conclusion: This case has clinical follow-up greater than 2 years post-operatively and could be a guide for treatment of a rare disorder with a substantial paucity of literature.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5887220PMC
http://dx.doi.org/10.1186/s13569-018-0092-zDOI Listing

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