AI Article Synopsis
- Ebstein's disease is a congenital issue with the tricuspid valve, leading to various blood flow problems based on its structure and other heart defects.
- A study involved 19 patients under 2 years old, with follow-ups ranging from 1 week to 16 years, averaging about 40 months.
- Out of the children, 8 died, 6 were lost to follow-up, and 5 survived; early cyanosis and other complications indicate a worse prognosis, but surviving the first year improves long-term outcomes.
Article Abstract
Ebstein's disease is a congenital malformation of the tricuspid valve that causes various hemodynamic alterations depending on the anatomic changes in the valve, presence or absence of atrial septal defect and reduction in the ventricular function. We present 19 patients with Ebstein's malformation of the tricuspid valve younger than 2 years of age. The long-term follow-up was from 1 week to 16 years with a mean of 40 months. Eight children died, 6 were lost in the follow-up and 5 survived. Early cyanosis with associated lesions give a bad prognosis. If the child survives the first year of life he has a better long term prognosis.
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