We report a case of a regenerative nodular hyperplasia with a portal vein cavernomatosis with a subsequent progression to symptomatic, occlusive thrombosis of the superior mesenteric vein. A thorough investigation resulted in a final diagnosis of primary myelofibrosis associated with the V617F mutation in the JAK2 gene.
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Article Synopsis
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- The research found that patients diagnosed incidentally had fewer liver-related complications and were more likely to have associated conditions compared to those diagnosed by clinical suspicion.
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