AI Article Synopsis
- Infantile desmoid fibromatosis is a rare, benign condition characterized by fibrous tissue growth in the postcricoid area, often leading to surgical challenges due to its tendency to recur and local infiltration.
- A 4-year-old boy with hoarseness and snoring for 2-4 years underwent ultrasound, revealing a lesion that affected laryngeal mobility, ultimately leading to a diagnosis made via surgery and histopathology.
- Following a local excision to alleviate airway narrowing, the boy experienced improvement in symptoms, but a residual lesion remained stable on follow-up imaging; ultrasonography is recommended as a useful non-radiative imaging tool alongside other methods for managing similar conditions.
Article Abstract
Rationale: Infantile desmoid fibromatosis of the postcricoid area is a rare disease and is characterized by a proliferation of fibrous tissue with non-metastasis, local infiltration, and a high rate of recurrence after surgical resection. Currently, ultrasound is scarcely used in the hypopharynx and larynx area.
Patient Concerns: A 4-year-old boy presented with hoarseness, deep voice and snoring for 2∼4 years without any surgical history. On sonography, the lesion was found in the postcricoid area, and the left larynx showed impaired mobility in real time observation. Complete excision with a negative margin in this pivotal anatomic area is impossible, and necessitates a long-time surveillance.
Diagnoses: Infantile desmoid fibromatosis of the postcricoid area was diagnosed according to surgery and histopathology.
Interventions: Local excision was carried out to relieve the upper airway narrowing.
Outcomes: Relieved hoarseness and snoring were reported on the latest follow-up. A residual lesion was seen in the surgical bed and maintained a stable extent on ultrasound and MR imaging after a year.
Lessons: Considering the non-radiation merit and diagnostic ability, ultrasonography is advocated as a valuable supplementary imaging method to CT, MR and laryngoscopy in the juvenile larynx and hypopharynx.
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Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5682829 | PMC |
| http://dx.doi.org/10.1097/MD.0000000000008500 | DOI Listing |
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