Transposition of the great arteries (TGA) is caused by discordance between the great arteries and the ventricles. If left untreated, this anomaly has a disastrous perspective. More recent surgical approach for correction includes the Lecompte technique in which the pulmonary bifurcation is transposed anterior to the aorta, which may be less physiologic. Although the early results are excellent, there is potential for future problems involving the great arteries and semilunar valves. These potential problems necessitate the development of other improved surgical techniques. Here we report an MRI 4D flow study related to a case of simple TGA whose primary surgical correction - direct spiral arterial switch operation (DSASO) - was performed twenty years ago in an attempt to restore physiologic arrangement among the great arteries and semilunar valves.
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http://dx.doi.org/10.21542/gcsp.2016.29 | DOI Listing |
Eur J Hum Genet
December 2024
National EDS Service, London North West University Healthcare NHS Trust, London, UK.
Vascular Ehlers-Danlos syndrome (vEDS) is a rare inherited connective tissue disorder predominantly caused by pathogenic COL3A1 variants. Characteristic arterial and intestinal fragility and generalised severe tissue friability can lead to clinical events from childhood. We highlight a paucity of literature regarding children diagnosed with vEDS, possibly explained by a restraint in predictive testing, and present data on 63 individuals (23 index cases) with a clinical and genetic diagnosis of vEDS in childhood (<18 years) to address this.
View Article and Find Full Text PDFJ Pediatr Surg
December 2024
Pediatric Surgery, Dipartimento di Medicina di Precisione e Rigenerativa a Area Jonica, Azienda Ospedaliera-Universitaria Consorziale Ospedale Pediatrico Giovanni XXIII, Bari, Italy.
Background And Aims: Image Defined Risk Factors (IDRFs) assess surgical risk in neuroblastoma (NB) and guide neoadjuvant therapy. Despite chemotherapy IDRFs may persist in 70 % of cases. Several studies have suggested that not all IDRFs hold equal significance and that the presence of an IDRF does not inherently signify unresectability.
View Article and Find Full Text PDFCirc Heart Fail
December 2024
Division of Pediatric Cardiology, Lucile Packard Children's Hospital, Stanford University School of Medicine, CA. (K.-J.L., D.H.).
Ann Vasc Dis
December 2024
Hanoi Medical University, Hanoi, Vietnam.
We report our hospital-based experience in management strategies and outcomes for pediatric extremity vascular trauma at a major trauma center. A retrospective chart review was conducted on patients under 18 with extremity vascular injuries who had surgery between May 2021 and February 2023. Among 46 children, 16 (34.
View Article and Find Full Text PDFAnn Vasc Dis
December 2024
Department of Plastic and Reconstructive Surgery, University of Tsukuba Hospital, Tsukuba, Ibaraki, Japan.
We present a case of arterial bypass for extensive stenosis of the ulnar artery and superficial palmar arch. The ulnar artery and the superficial palmar arch were bypassed using the great saphenous vein. Postoperatively, blood flow to the affected fingers gradually improved and the pain disappeared.
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