A 37-year-old South-Asian male presented to our clinic with a crusty, verrucous-like, scaly plaque of the left ala of the nose. After ruling out infectious and other epidermal bullous diseases, we finalized a diagnosis of localized pemphigus foliaceus, an exceptionally rare disorder with only 15 cases reported in the literature to date. The hyperkeratotic lesions responded favorably to a 3-week regimen of triamcinolone ointment and a onetime intralesional triamcinolone 2.5 mg/mL injection.
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| http://dx.doi.org/10.1159/000477959 | DOI Listing |
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Article Synopsis
- Pemphigus foliaceus is an autoimmune skin disorder that causes superficial blisters.
- Localized cases are extremely rare, with very few documented instances.
- This report describes the first known case of an 81-year-old man with localized pemphigus foliaceus that appeared as dermatomal facial lesions, highlighting the diagnostic challenges due to its atypical presentation.
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