Purpose: To describe a 42-year-old man, a known case of Bietti crystalline dystrophy who underwent surgery for unilateral full thickness macular hole.

Case Report: Clinical features, color fundus photographs, and optical coherence tomography, electroretinography, and electrooculography findings of the patient are reported. His visual acuity improved from counting fingers to 20/50 after pars plana deep vitrectomy with internal limiting membrane (ILM) peeling and gas injection.

Conclusion: Macular hole can occur in Bietti crystalline dystrophy and the post-surgical outcome is good.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5525505PMC
http://dx.doi.org/10.4103/jovr.jovr_154_15DOI Listing

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