Cardiac amyloidosis is a manifestation of amyloidosis which is a multisystem disorder. This is difficult to diagnose, rare disease which eventually leads to the mortality. Diagnosis requires a high index of clinical suspicion along with echocardiographic clues like, diastolic dysfunction, bi-atrial enlargement and ventricular thickening. Treatment is mainly supportive with disappointing outcomes. We present a case of systemic amyloidosis with negative congo red staining, presenting with predominantly cardiac features.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5449843 | PMC |
| http://dx.doi.org/10.7860/JCDR/2017/24698.9661 | DOI Listing |
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