Ophthalmological manifestations of Von Recklinghausen disease are rare. Only a few cases have been reported in the international literature. We here report the case of a patient with pulsatile exophthalmos revealing spheno-orbital agenesis associated with Von Recklinghausen's disease.
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| http://dx.doi.org/10.11604/pamj.2016.25.104.9006 | DOI Listing |
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