The syndrome of Klippel-Trenaunay, a polyvalent angiodysplasia.

J Cardiovasc Surg (Torino)

Department of Cardiothoracic and Vascular Surgery, University of Bern Medical School, Switzerland.

Published: October 1987

The syndrome of Klippel and Trenaunay remains basically a venous angiodysplasia. Newer investigative methods have however allowed us to distinguish a polyvalence of the vascular morphology. The basic clinical triad: vascular nevus, varicosities and limb hypertrophy remains the main clinical diagnostic characteristic.

Download full-text PDF

Source

Publication Analysis

Top Keywords

syndrome klippel-trenaunay
4
klippel-trenaunay polyvalent
4
polyvalent angiodysplasia
4
angiodysplasia syndrome
4
syndrome klippel
4
klippel trenaunay
4
trenaunay remains
4
remains basically
4
basically venous
4
venous angiodysplasia
4

Similar Publications

Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular disorder involving varicosities, cutaneous vascular malformations, and hypertrophy of soft tissues and bones. It is often linked to gene mutations. It affects the lymphatic, capillary, and venous systems.

View Article and Find Full Text PDF

Gastrointestinal bleeding resulting from the involvement of the gastrointestinal tract in people with Klippel-Trenaunay syndrome (KTS) is exceedingly uncommon and frequently neglected. A 22-year-old male, a diagnosed case of KTS, was assessed for per rectal bleeding and abdominal discomfort. A colonoscopy revealed third-degree hemorrhoids with vascular malformation all over the colon.

View Article and Find Full Text PDF

Introduction: Klippel-Trenaunay Syndrome (KTS) is a rare congenital condition characterized by vascular malformations, bone abnormalities, and limb overgrowth. The genetic basis of KTS is not fully understood, and the diagnosis relies on clinical features. Its clinical spectrum includes several neurosurgical diagnoses, such as cavernous hemangiomas, arteriovenous fistulas, and Chiari I malformation.

View Article and Find Full Text PDF

Background: The lower limb venous system, a subject of extensive study due to its high clinical significance on deep vein thrombosis, presents a rare, intriguing, symmetrical variant in this dissection report.

Case Report: We present the uncommon and clinically meaningful bilateral persistent sciatic vein (PSV) variant. The developmental variant was symmetrically detected during a dissection of an 81-year-old female donated cadaver.

View Article and Find Full Text PDF

Introduction: Klippel-Trenaunay Syndrome (KTS) is a medical condition that involves the abnormal enlargement of bones and soft tissues, along with the presence of arterio-venous malformations and cutaneous vascular nevus. This is an uncommon condition that is present from birth and affects the blood vessels. There are relatively few documented cases of how to treat fractures in the lower limbs of individuals with this condition.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!