Perioperative considerations in infantile neuroaxonal dystrophy.

Paediatr Anaesth

Department of Anesthesiology, Perioperative and Pain Medicine, Boston Children's Hospital, Boston, MA, USA.

Published: March 2017

AI Article Synopsis

  • Infantile neuroaxonal dystrophy is a severe, fatal neurological disorder, leading to a life expectancy of less than 10 years.
  • A 10-year-old affected boy had a successful posterior spinal fusion after halo traction, with recovery allowing for extubation by day 3 post-surgery.
  • The surgery raised specific perioperative concerns, particularly regarding difficult intubation and potential respiratory issues due to the boy's condition.

Article Abstract

Infantile neuroaxonal dystrophy is a rare neurological disorder that is universally fatal with life expectancy under 10 years. A 10-year-old boy with infantile neuroaxonal dystrophy and severe neuromuscular scoliosis underwent posterior spinal fusion following halo traction. He was successfully extubated to bilevel positive airway pressure on postoperative day 3 and discharged home on postoperative day 11. Infantile neuroaxonal dystrophy presents several perioperative challenges including concerns for difficult intubation and respiratory dysfunction.

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Source
http://dx.doi.org/10.1111/pan.13081DOI Listing

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