Tumid lupus: An unexpected diagnosis for the otolaryngologist.

Am J Otolaryngol

Department of Pathology, University of Illinois Hospital and Health Sciences System, 840 S. Wood Street, CSN 130, Chicago, IL 60612, United States. Electronic address:

Published: December 2017

Tumid lupus is an uncommon variant of lupus erythematosus. Patients present with subcutaneous lesions. Ophthalmic literature reports disease manifestation as orbital inflammation. Autoimmune serology is often negative. Without a high index of suspicion, the diagnosis is easily overlooked delaying treatment. Tumid lupus is not significantly discussed in the Otolaryngologic literature. Here we present a Case Report of a male who initially presented to Ophthalmology with unilateral orbital complaint of eyelid puffiness. Orbital biopsy and subsequent biopsy of his submental skin lesions ultimately led to this unexpected diagnosis. We discuss the method to diagnose tumid lupus including representative histopathologic findings.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5826658PMC
http://dx.doi.org/10.1016/j.amjoto.2017.01.003DOI Listing

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