Cystic Pheochromocytoma Presenting as Adrenal Cyst.

J Clin Diagn Res

Senior Medical Specialist, GB Pant Hospital, Port Blair, Andaman and Nicobar Islands, India .

Published: November 2016

Pheochromocytomas are usually solid tumours. But it can present as cystic lesions in the adrenal gland. Cystic lesions in adrenal gland with hypertension needs attention to rule out pheochromocytoma. If ignored, it may lead to hypertensive emergency, multisystem crisis and death. Early diagnosis with biochemistry, Computed Tomography (CT) or Magnetic Resonance Imaging (MRI) of abdomen, proper functional imaging like Meta Iodo Benzyl Guanidine (MIBG) scan is essential. Proper preoperative preparation is important to prevent hypertensive crisis during and after surgery. We are reporting a case of cystic pheochromocytoma in a young male.

Download full-text PDF

Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5198380PMC
http://dx.doi.org/10.7860/JCDR/2016/20129.8892DOI Listing

Publication Analysis

Top Keywords

cystic pheochromocytoma
8
cystic lesions
8
lesions adrenal
8
adrenal gland
8
cystic
4
pheochromocytoma presenting
4
presenting adrenal
4
adrenal cyst
4
cyst pheochromocytomas
4
pheochromocytomas solid
4

Similar Publications

New Developments in VHL-Associated Neuroendocrine Neoplasms.

Curr Oncol Rep

January 2025

Neuroendocrine Tumour Unit, ENETS Centre of Excellence, 1st Department of Propaedeutic and Internal Medicine, Laiko Hospital, National and Kapodistrian University of Athens, Agiou Thoma 17, Athens, 11527, Greece.

Purpose Of Review: The purpose of this review is to outline the current knowledge on epidemiology, diagnosis and management of neuroendocrine neoplasms (NENs) that develop in the context of Von Hippel-Lindau (VHL) syndrome.

Recent Findings: Pancreatic NENs develop in 8-17% of VHL patients (vPNENs) and are mostly multi-focal, cystic and non-functioning. Surgical resection is recommended for vPNENS > 3 cm that exhibit higher metastatic potential or in tumors with short doubling time while in the 20% of cases with metastatic disease the HIF-2 A inhibitor belzutifan is considered a promising option.

View Article and Find Full Text PDF

Introduction: Although giant cystic pheochromocytoma and paraganglioma (PPGL) are uncommon, they can be life-threatening when it occurs. Unfortunately, prior case reports have shown that giant cystic PPGLs are highly susceptible to diagnostic errors. Therefore, this study aimed to explore giant cystic PPGLs by comparing them with non-cystic PPGLs, defining the clinical features of the affected patients, and analyzing the characteristics of misdiagnosis and mistreatment associated with PPGLs.

View Article and Find Full Text PDF
Article Synopsis
  • Adrenal masses include various abnormal growths in the adrenal gland, with pseudocysts being the most common type of cysts; there are currently no specific guidelines for their management due to their rare occurrence.
  • A systematic review of 39 studies from 2000 to 2023 focused on the clinical and radiological characteristics of adrenal gland pseudocysts, analyzing data from 45 patients, primarily adult women.
  • Findings indicated that many patients were asymptomatic or experienced vague abdominal pain, with the most notable imaging result being cystic lesions with calcifications; surgical intervention was necessary in cases of compression, growth, or cancer suspicion, with a majority undergoing open surgery.
View Article and Find Full Text PDF

Pheochromocytoma is a rare neuroendocrine tumor arising from adrenal medulla. Patients usually show classic triad of headache, palpitations and diaphoresis along with persistent or paroxysmal hypertension. Majority of the tumors are solid or mixed solid and cystic.

View Article and Find Full Text PDF

Late-Onset Manifestations of Von Hippel-Lindau Syndrome: A Case Report.

Cureus

June 2024

Radiology, Dr. D. Y. Patil Medical College, Hospital and Research Centre, Dr. D. Y. Patil Vidyapeeth, Pune (Deemed to be University), Pune, IND.

Von Hippel-Lindau (VHL) syndrome is characterized by a range of tumors including phaeochromocytomas, pancreatic adenomas, cerebellar haemangioblastomas, and renal cell carcinomas. A 50-year-old male presented with a three-week history of headache. Additionally, the patient exhibited signs of hypertension.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!