Objective: To assess the importance of management and close follow-up of patients with tuberous sclerosis that associate renal angiomyolipomas.
Methods: To report a case.
Results: A 55 years old men with tuberous sclerosis diagnosed in childhood and later finding of bilateral giant renal masses in imaging studies, with significant compromise of renal function. The patient did not have a proper follow up and did not receive any treatment. At the moment he has end stage kidney disease.
Conclusion: Patients that associate renal angiomyolipoma and tuberous sclerosis, have specific characteristics with a higher risk of complications requiring strict follow-up and specific treatment.
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