Limited Wegener's Granulomatosis Presenting with an Isolated Abduction Deficit.

Neuroophthalmology

Department of Ophthalmology and Visual Sciences; Department of Neurology, University of IowaIowa City, IowaUSA; Department of Neurology, Veterans Affairs Medical CenterIowa City, IowaUSA.

Published: April 2014

Wegener's granulomatosis often affects the orbit, typically presenting with painful proptosis. The authors describe a 14 year-old girl, with limited Wegener's granulomatosis, who initially presented with an isolated painless abduction deficit that spontaneously resolved over several weeks. She subsequently developed painful proptosis and diplopia, followed by facial and oral nodules. This case demonstrates that limited Wegener's granulomatosis can rarely present with an isolated painless abduction deficit.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5122943PMC
http://dx.doi.org/10.3109/01658107.2014.894086DOI Listing

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