Synovial sarcoma of the hypopharynx in a pediatric patient: Case report.

Int J Surg Case Rep

Department of Otorhinolaryngology - Head & Neck Surgery, Geneva University Hospital, 4, rue Gabrielle Perret-Gentil, 1204 Geneva, Switzerland.

Published: September 2016

Introduction: Synovial sarcoma (SS) is uncommon high grade soft tissue sarcoma, accounting for less than 10% of all head and neck sarcomas. Also, about 10% of SS occur within the Head & Neck. In the pediatric population, SS is an extremely rare head & neck malignancy.

Presentation Of Case: We present a case of sixteen years old boy diagnosed with SS situated of the hypopharynx treated by surgical excision and post operative radio-chemotherapy.

Discussion: This anatomical location brings additional functional challenges (swallowing, phonation, respiration), especially in the pediatric population. Pre-operative and even post-operative histopathological diagnosis of SS remains difficult. Optimal treatment of Head & Neck SS has to balance functional and oncologic aspects.

Conclusion: SS is an extremely rare head & neck malignancy in pediatric population. It has multifaceted challenges including pre and post-operative histopathological diagnosis and optimal modality of treatment. Clinical judgment, especially in the pediatric population, needs to balance tumor free margins and organ preservation in head and neck region.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC5031474PMC
http://dx.doi.org/10.1016/j.ijscr.2016.08.043DOI Listing

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