The basioccipital skull base is an extremely rare site for meningoencephalocele. The herniation of the brainstem or part of it through a basioccipital defect is even rarer. We report a case of rhombencephalomeningocele associated with a tethered dermoid. An extensive literature search revealed no such case report of basioccipital cranial dysraphism so far presenting with cranial nerve palsy.
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.1159/000446400 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Detailed analysis of cystic lesions in patients after open fetal repair and postnatal myelomeningocele closure.
Childs Nerv Syst
January 2025
Division of Neurosurgery, Department of Surgery, Children's Hospital of Philadelphia, Philadelphia, PA, USA.
Purpose: We sought to evaluate the incidence, natural history, and management of cystic spinal lesions following myelomeningocele/myeloschisis closure.
Methods: We performed a single-center retrospective review of all patients who underwent myelomeningocele/myeloschisis closure from 2013 to 2018 with follow-up to 5 years old.
Results: We analyzed 100 fetal repairs and 81 postnatal closures from 305 total surgeries.
The importance of timing: evaluating the optimal age for surgical intervention in asymptomatic dermal sinus tracts.
J Neurosurg Pediatr
November 2024
1Department of Neurosurgery, Children's National Medical Center.
Article Synopsis
- Dermal sinus tracts (DSTs) are rare congenital lesions that pose risks of infection and neurological issues due to their connection between the skin and spinal cord, making surgical intervention recommended, though the timing for surgery in asymptomatic cases is uncertain.
- A retrospective review from 1998 to 2022 studied 52 patients who underwent DST excision and detethering, excluding those with pre-existing complications.
- Results indicated a median surgery age of 7 months, with complications in 8% of cases, and younger age at surgery was linked to higher risks of postoperative problems and continued neurological issues.
Diastematomyelia with tethered cord and concurrent distal cord intramedullary dermoid cyst: A case report.
Radiol Case Rep
December 2024
Radiology Department, French Medical Institute for Mothers and Children (FMIC), Kabul, Afghanistan.
Article Synopsis
- - Diastematomyelia is a rare birth defect where the spinal cord divides into two halves, potentially leading to complications.
- - The case focuses on a 5-year-old boy who has type 2 diastematomyelia along with a dermoid cyst located in the lower part of his spinal cord.
- - MRI was used to diagnose the condition, and the patient underwent surgery to treat both the diastematomyelia and the dermoid cyst.
Tethered cord prevalence among patients with prenatal or postnatal myelomeningocele repair.
Childs Nerv Syst
November 2024
Department of Neurological Surgery, Montefiore Medical Center and the Albert Einstein College of Medicine, Bronx, NY, 10467, USA.
Article Synopsis
- - The study investigates outcomes of prenatal versus postnatal surgical repair of myelomeningocele (MMC), a severe form of spina bifida, focusing on factors like spinal cord tethering and other complications.
- - A total of 18 patients were reviewed from 2002 to 2020, with equal groups for prenatal and postnatal repair, and demographic data collected included age, sex, and medical history.
- - Results showed that patients who had prenatal closure experienced fewer detethering procedures and lower rates of requiring a ventriculoperitoneal shunt compared to those with postnatal repair, highlighting potential benefits of prenatal surgery.
Diastematomyelia, tethered cord, intradural extramedullary dermoid tumor and lipomyelomeningocele such disease entities themselves are rare in their own form and concurrent presentation of all those pathological states in a single individual can be considered one of the rarest forms of spinal dysraphism globally. Moreover for prompt management with optimal prognosis needs refined neurosurgical intervention guided by intraoperative neuromonitoring so as to bring about the best quality of life in the patient.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!