Classical presentation of Gardner's syndrome in an Indian patient: A case report.

Contemp Clin Dent

Department of Oral Medicine and Radiology, Government Dental College and Hospital, Mumbai, Maharashtra, India.

Published: June 2016

Gardner's syndrome is an autosomal dominant disease characterized by the presence of colonic polyposis, osteomas, and a multitude of soft-tissue tumors. Dental anomalies are present in estimated 30% of all affected individuals of Gardner's syndrome, so dental professionals play an important role in determining the early signs of the syndrome. The intestinal polyps have a 100% risk of undergoing malignant transformation if not treated thus, early diagnosis and regular surveillance are important. In this report, we describe classical presentation of Gardner's syndrome in a patient who presented with bilateral swellings on palate along with multiple impacted teeth.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4906882PMC
http://dx.doi.org/10.4103/0976-237X.183063DOI Listing

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