Coronary artery bypass graft in a patient with Fabry's disease.

Cardiovasc Pathol

Department of Pathology, Mitsubishi Kyoto Hospital, 1 Katsuragoshomachi, Nishikyo-ku, Kyoto, 615-8087, Japan.

Published: January 2017

Fabry's disease is a lysosomal storage disease characterized by intracellular accumulation of ceramide trihexoside resulting from alpha-galactosidase A deficiency. While the heart is often involved, coronary artery disease and its management in Fabry's disease patients are extremely rare clinical entities. We report a case of a 72-year-old man with left main disease in Fabry's disease with special consideration of the arterial wall pathology.

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Source
http://dx.doi.org/10.1016/j.carpath.2016.04.002DOI Listing

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