AI Article Synopsis
- Gorham's disease, also known as vanishing bone disease, is a rare disorder that leads to the gradual loss of bone and its replacement with fibrous tissue, with common areas affected including the shoulder and pelvis.
- The disease doesn't favor any specific age, gender, or race, and around 50 cases with involvement of the jaw have been documented.
- Although the cause is unknown and symptoms can vary, the overall prognosis is good unless vital body parts are affected; there is no established treatment protocol due to its rarity.
Article Abstract
Gorham's disease or vanishing bone disease is a rare, progressive musculoskeletal disorder characterized by resorption of bone matrix, and later replaced by fibrous connective tissue. The disease has no specific predilection for age, gender, or race. The most common sites of involvement are the shoulder and pelvic bones. To date, nearly 50 cases of Gorham's disease with maxillofacial involvement have been reported in the literature. The etiology of Gorham's disease is not known, clinical features are variable, and prognosis is generally good unless vital structures are involved. Due to the rarity of the condition, no definite treatment protocol exists for this disorder. Here, we described a pediatric case of Gorham's disease with mandibular involvement.
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| http://dx.doi.org/10.4103/0970-4388.180450 | DOI Listing |
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