AI Article Synopsis

  • Hypertrophic cardiomyopathy (HCM) is a common inherited heart condition affecting about 1 in 500 people, leading to heart muscle thickening and potential severe complications like sudden cardiac death.
  • Echocardiography is essential for diagnosing and monitoring patients with HCM, as standard methods may miss critical details specific to this condition.
  • The British Society of Echocardiography has set guidelines for additional imaging and measurements to better assess and predict outcomes in patients with known or suspected HCM.

Article Abstract

Hypertrophic cardiomyopathy (HCM) is a relatively common inherited cardiac condition with a prevalence of approximately one in 500. It results in otherwise unexplained hypertrophy of the myocardium and predisposes the patient to a variety of disease-related complications including sudden cardiac death. Echocardiography is of vital importance in the diagnosis, assessment and follow-up of patients with known or suspected HCM. The British Society of Echocardiography (BSE) has previously published a minimum dataset for transthoracic echocardiography, providing the core parameters necessary when performing a standard echocardiographic study. However, for patients with known or suspected HCM, additional views and measurements are necessary. These additional views allow more subtle abnormalities to be detected or may provide important information in order to identify patients with an adverse prognosis. The aim of this Guideline is to outline the additional images and measurements that should be obtained when performing a study on a patient with known or suspected HCM.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4676492PMC
http://dx.doi.org/10.1530/ERP-14-0115DOI Listing

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