AI Article Synopsis
- Brugada syndrome is a rare hereditary condition characterized by specific electrocardiographic changes and a heightened risk of sudden death from ventricular fibrillation, predominantly in males.
- Symptoms include fainting, sudden cardiac death, and abnormal heart rhythms, often visible during electrophysiological testing.
- Diagnosis involves observing a distinct ECG pattern, and in the cases presented, both patients were treated with an implantable cardioverter-defibrillator (ICD).
Article Abstract
Brugada syndrome is a rare hereditary condition comprising electrocardiographic findings and an increased risk of sudden death due to ventricular fibrillation. The transmission is autosomal dominant with incomplete penetrance, mainly affecting males. The clinical manifestations include syncope, sudden cardiac death, nocturnal agonal breathing, documented ventricular tachycardia/fibrillation, and inducibility of arrhythmias during electrophysiologial study. The ECG should typically have an appearance of a right bundle branch block with a coved ST-segment elevation ≥ 2 mm, followed by a negative T-wave, in at least one right-sided lead (V1-V2). Two cases of Brugada syndrome are hereby presented, both of whom received the definitive treatment - ICD.
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