The authors have studied the course and the efficacy of the surgical treatment of the hemimelic form of epiphyseal dysplasia in 15 children. Three roentgenologic types of epiphysis lesions have been distinguished. It has been determined that the pathologic changes are mainly localized in the posterior medial departments. In multiple severe lesions hyperfunction of the growth areas followed by their early asymmetric synostosis with the development of secondary deformations and focal disturbances in the ossification of the metaphyses have been observed. The necessity of early surgical treatment allowing to prevent the development of the pathologic changes in the growth areas and deforming arthrosis has been substantiated.
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J Orthop Case Rep
September 2020
Department of Orthopaedics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Introduction: Melorheostosis, on its own, is an extremely uncommon disease. It is non-hereditary, sclerosing bone lesion affecting the adjacent soft tissues. Long bones are commonly involved.
View Article and Find Full Text PDFCase Rep Orthop
May 2017
Orthopaedic and Traumatology Department, S. Andrea Hospital, Faculty of Medicine and Psychology, "Sapienza" University of Rome, Rome, Italy.
The dysplasia epiphysealis hemimelica (DEH) is a rare disease of unknown etiology consisting in an abnormal osteocartilaginous growth at the epiphysis, usually hemimelic with histological findings similar to benign osteochondroma. In this case series, we described the results of the arthroscopic treatment of 2 consecutive cases of intra-articular ankle localization of DEH in 2 patients aged 9 and 10 years. The good result obtained, persistent at the 5-year follow-up, leads us to consider the arthroscopic approach as a reliable treatment in patient affected by intra-articular ankle DEH.
View Article and Find Full Text PDFSkeletal Radiol
January 2017
School of Medicine, Pathology Department, Gaziosmanpasa University, Tokat, Turkey.
Dysplasia epiphysealis hemimelica (DEH) is a rare developmental disorder characterized by osteocartilaginous overgrowth in one or more epiphyses. The disease usually involves a single limb or is hemimelic (lateral or medial compartment), and lower extremities are more frequently affected than upper extremities. Here we present clinical and radiological findings for a male DEH patient at 1.
View Article and Find Full Text PDFJ Pediatr Orthop B
November 2017
Departments of aOrthopaedics and Trauma bRadiodiagnostic, Antalya Memorial Hospital cOrthopaedics and Trauma Department, Akdeniz University School of Medicine, Antalya dOrthopaedics and Trauma Department, Ozel Bahar Hospital, Bursa, Turkey.
Trevor's disease, also known as dysplasia epiphysealis hemimelica, is a rare nonhereditary skeletal development disorder that affects epiphyses. This type of dysplastic lesion was first reported by Mouchet and Berlot in 1926 under the name 'tarsomegaly'. The main aim of this study is to raise awareness of Trevor's disease among orthopedic surgeons and underline some important aspects of treatment by a detailed presentation of four different possible manifestations of the disease.
View Article and Find Full Text PDFOrthop Traumatol Surg Res
December 2014
Department of Pediatric Orthopaedics Surgery, University hospital of Montpellier, 34295 Montpellier, France. Electronic address:
Background: Dysplasia epiphysealis hemimelica (DEH) is a rare developmental bone disorder with hemimelic involvement of one or more epiphysis. We report on nine new cases and discuss the clinical manifestations, the value of MRI, and the results of complete and early surgical resection of these lesions.
Materials And Methods: In this retrospective study, nine patients with a diagnosis of DEH were evaluated.
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